Keywords
Enfermedad de Wegener
Hemorragia alveolar
Neumonía
SDRA Acute granulomatous poliangiitis
Wegener’s disease
Alveolar bleeding
Pneumonia
ARDS
How to Cite
Abstract
Acute Granulomatous Polyangiitis (AGPA), known as Wegener,’s granulomatosis, is a rare and multi-systemic disease that causes medium and small vessel inflammation. It appears initially during adolescence from 15 to 16 years of age, affecting primarily the upper respiratory tract, the lungs and kidneys. This is the case of a male, 15 year old symptomatic and paraclinical tests suggestive of pneumonia; the patient evolved to ARDS and diffuse refractory alveolar bleeding.
References
Ananthakrishnan Lakshmi, Sharma Nidhi, Kanne Jeffrey P. Wegener's Granulomatosis in the Chest: High-Resolution CT Findings. AJR:192, March 2009. https://doi.org/10.2214/AJR.08.1837
Chernick Victor. Pulmonary vasculitides in children. Paediatric Respiratory Reviews (2006) 7S, S243-S244. https://doi.org/10.1016/j.prrv.2006.04.190
McDonagh JE, Jordan AC. Transitional care for young people with Connective tissue diseases. Paediatrics and Child Health 20:2. 2009; 79-82. https://doi.org/10.1016/j.paed.2009.09.010
Khan A.M; Elahi F; Hasmi S.R Wegener's granulomatosis: A rare, chronic, and multisystem disease. The royal college of surgeons of Edinburgh and Ireland. Surgeon 4: 1,45-52. 2006. https://doi.org/10.1016/S1479-666X(06)80021-1
Lohrmann Christian, Uhl Markus, Kotter Elmar, et al. Pulmonary manifestations of wegener granulomatosis: CT findings in 57 patients and a review of the literature. European Journal of Radiology 53 (2005) 471-477. https://doi.org/10.1016/j.ejrad.2004.04.016
Ioachimescu Octavian C., Stoller James K. Diffuse alveolar hemorrhage: Diagnosing it and finding the cause. Cleveland Clinic Journal of Medicine. Volume 75 number 4 april 2008. https://doi.org/10.3949/ccjm.75.4.258
Hernandorena González Marta, Bértolo Domínguez Marta, Dosdá Muñoz Rosa, et al. Vasculitis de Wegener: diferentes presentaciones pulmonares en el diagnóstico inicial y durante la evolución de la enfermedad. Servicio de Radiodiagnóstico, Hospital Clínico Universitario. Valencia. España. RAR Volumen 73 Número 3, (2009) 277-280.
Leatherman James W. Review Immune Alveolar Hemorrhage. CHEST /91/6 JUNE, 1987. 891. https://doi.org/10.1378/chest.91.6.891
Morales-Angulo Carmelo, García-Zornoza Roberto, Obeso-Agüera Sergio, et al. Ear, Nose and Throat Manifestations of Wegener's Granulomatosis (Granulomatosis With Polyangiitis). Acta Otorrinolaringol Esp. 2012;63(3):206-211. https://doi.org/10.1016/j.otoeng.2012.05.004
Martín-Suñé Natalia y Juan José Ríos-Blanco. Afectación pulmonar de las vasculitis. Servicio de Medicina Interna, Hospital Universitario La Paz, Madrid, España. Arch Bronconeumol. 2012;48 (11):410-418. https://doi.org/10.1016/j.arbres.2012.04.007
.Rosai, J. Rosai and Ackerman's Surgical Pathology.Volumen 1-2. 2011.
Rajesh Thomas, Devasahayam J. Christopher, Anita Madan. Department of Pulmonary Medicine. The Christian Medical College, Vellore, Tamilnadu, India. Respiratory Medicine Extra (2005) 1, 43-46. https://doi.org/10.1016/j.rmedx.2005.04.001
Castro Aldana Mayra Sofía, Villagómez Ortiz Asisclo de Jesús, Hernández Silva Saúl. Hemorragia alveolar difusa en pacientes críticos: casos clínicos y revisión de la literatura. Med Int Mex 2007;23:159-71.