Palabras clave
McCune-Albright
Displasia fibrosa
Niñez Syndrome
McCune-Albright
Fibrous displasia
Childhood
Cómo citar
Resumen
La displasia fibrosa es una enfermedad ósea benigna en la que el hueso normal es reemplazado por tejido fibroso, cuando se asocia con trastornos endocrinológicos y de hiperpigmentación en la piel se denomina síndrome de McCune-Albright. Presentamos un caso poco frecuente de síndrome de McCune-Albright en una niña de cinco años de edad con lesiones de la piel y compromiso difuso unilateral de las articulaciones.
Citas
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